摘要：Ataxia cerebelar type II, also known by ataxia spinocerebelar 7 (SCA7), it is a neuro-degenerative pathology with gloomy prognostic of hereditariness. It attacks both sexes and in any age, being characterized by the variable degeneration of the cortex cerebelar, inferior olive, pontine nuclei, basal ganglion, spinal strings and outlying nerves. The people dont die for the disease in itself but for the associated clinical complications. Exploratory study, that had for objective: to identify the deficits of family knowledge concerning the ataxia II, establishing the repercussions of these in the life quality of the carriers. As population was chosen the relatives of ataxia carriers that are part of the Beneficent Association in Prol of Ataxia IIS Carriers (ABPAT), with in Crateús, Ceará. The sample consists of sixteen people, being 12 women and 04 men. The data collect took place during the months of March, April and May 1999, having been used questionnaire contends open and shut questions. Without cure perspectives, the great weapon of the family, still, is the information in what refers to the precocious detection, to the retard of the symptoms evolution and prevention of the appearance of associated problems it was Ended, though, to be common to existence of more than a symptomatic carrier in the interviewees family, and this fact can have great relationship with the little conscientiousness concerning the genetic transmission and of as the most recent generations they can suffer more intensely of the effects of that problematic one.
其他摘要：Ataxia cerebelar type II, also known by ataxia spinocerebelar 7 (SCA7), it is a neuro-degenerative pathology with gloomy prognostic of hereditariness. It attacks both sexes and in any age, being characterized by the variable degeneration of the cortex cerebelar, inferior olive, pontine nuclei, basal ganglion, spinal strings and outlying nerves. The people dont die for the disease in itself but for the associated clinical complications. Exploratory study, that had for objective: to identify the deficits of family knowledge concerning the ataxia II, establishing the repercussions of these in the life quality of the carriers. As population was chosen the relatives of ataxia carriers that are part of the Beneficent Association in Prol of Ataxia IIS Carriers (ABPAT), with in Crateús, Ceará. The sample consists of sixteen people, being 12 women and 04 men. The data collect took place during the months of March, April and May 1999, having been used questionnaire contends open and shut questions. Without cure perspectives, the great weapon of the family, still, is the information in what refers to the precocious detection, to the retard of the symptoms evolution and prevention of the appearance of associated problems it was Ended, though, to be common to existence of more than a symptomatic carrier in the interviewees family, and this fact can have great relationship with the little conscientiousness concerning the genetic transmission and of as the most recent generations they can suffer more intensely of the effects of that problematic one.
关键词：Ataxia cerebelar;Cuidados de enfermagem;Cerebelar ataxia;Nursing care;Ataxia cerebelar;Cuidados de enfermagem
