文章基本信息
- 标题：Three Cases of Outer Retinal Tubulation in Bietti's Crystalline Dystrophy
- 本地全文：下载
- 作者：Kim, Yong Il ; Kim, In Taek ; Kim, Jin Seon 等
- 期刊名称：Journal of the Korean Ophthalmological Society
- 印刷版ISSN：0378-6471
- 出版年度：2015
- 卷号：56
- 期号：7
- 页码：1141-1148
- DOI：10.3341/jkos.2015.56.7.1141
- 语种：Korean
- 出版社：The Korean Ophthalmological Society
- 摘要：Purpose
To report the prevalence and the characteristics of outer retinal tubulation (ORT) in Bietti's crystalline dystrophy in 6 eyes of 3 patients.
Case summaryThree patients with Bietti's crystalline dystrophy were examined using color fundus photography, fundus autofluorescence picture, spectral domain optical coherence tomography (SD-OCT), fluorescein angiography, electroretinogram and electrooculogram. ORT was detected in 3 of 3 (100%) Bietti's crystalline dystrophy patients. SD-OCT B-scan revealed hyperreflective material inside the hyporeflective internal space with hyperreflective border. ORT was observed under the fovea or outside the fovea and on the outer nuclear layer in the retina. ORTs were no greater than 70 × 140 µm in size when measured using SD-OCT B-scan image.
ConclusionsORT was observed frequently in patients with Bietti's crystalline dystrophy. These findings can potentially predict the extensive photoreceptor abnormalities in retinal pigment epithelial atrophy.
- 关键词：Bietti\'s crystalline dystrophy; Outer retinal tubulation; Spectral domain optical coherence tomography
