摘要：Müllerian malformations result from defective fusion of the Müllerian ducts during development of the femalereproductive system. The least common form of these malformations is Herlyn-Werner-Wunderlich syndromecharacterized by obstructed hemivagina and ipsilateral renal anomaly (OHVIRA). The most common presentationof this syndrome is a mass secondary to hematocolpos, pain, and dysmenorrhea. Clinical diagnosis is verychallenging and requires imaging studies in which ultrasound and MRI play an essential role in the diagnosis,classification and treatment plan.We report two cases of this syndrome, featuring two very rare clinical presentations: hematosalpinx and pyocolpos.The clinical course of the pathology is not standard and each patient is treated accordingly.
