Spinal muscular atrophy (SMA) is a rare lower motor neuron disease without sensory loss that needs special care of anesthesiologists due to increased sensitivity to muscle relaxants, potential for aspiration and respiratory weakness. We anesthetized a 10 year-old girl with type 3 SMA for resection of sebaceous cyst in her occiput. We used intravenous anesthetic technique and intubated the patient without any muscle relaxants. The anesthetic and recovery courses were successful. So we present our general anesthetic case under the endotracheal intubation without any muscle relaxants as one of the anesthetic methods for the patients with SMA.