Poland syndrome is a rare congenital anomaly characterized by unilateral chest wall hypoplasia and ipsilateral upper extremity abnormalities, usually on the right side. It can be combined with other anomalies such as scapular deformity of the affected side, and hypoplasia or absence of nipple. Typical surgery for a Poland syndrome patient aims to correct the chest wall defect and/or other abnormalities. Ventilation problem such as paradoxical chest movement can occur during anesthesia. We report management of general anesthesia of a Poland syndrome patient with right chest wall defect undergoing inframammary fold reposition and liposuction.