首页    期刊浏览 2024年11月24日 星期日
登录注册

文章基本信息

  • 标题:Secondary renal amyloidosis in a 13-year-old girl with bronchiectasis
  • 本地全文:下载
  • 作者:Yang, Eun Ae ; Lee, Dong Won ; Hyun, Myung Chul
  • 期刊名称:Korean Journal of Pediatrics
  • 印刷版ISSN:1738-1061
  • 出版年度:2010
  • 卷号:53
  • 期号:7
  • 页码:770-773
  • DOI:10.3345/kjp.2010.53.7.770
  • 语种:English
  • 出版社:The Korean Pediatric Society
  • 摘要:

    A 13-year-old girl was diagnosed with non-cystic fibrosis (CF)-related multifocal bronchiectasis accompanied by nephrotic-range proteinuria of unknown cause. On renal biopsy, there were many segmental homogeneous deposits of amyloid tissue with positive Congo red staining in the glomeruli and interstitium. On electron microscopy, relatively straight, non-branching, randomly arranged amyloid fibrils were showed in the mesangium of the glomeruli. These fibrils were approximately 10 nm in diameter, compatible with secondary amyloidosis. Her level of serum amyloid A was remarkably elevated. To our knowledge, this girl is the first case of secondary renal amyloidosis induced by bronchiectasis in Korean children.

  • 关键词:Amyloidosis; Bronchiectasis
国家哲学社会科学文献中心版权所有