1.Enzyme replacement therapy in Gaucher's disease: large-scale purification of glucocerebrosidase suitable for human administration

作　　者：F S Furbish ;H E Blair ;J Shiloach 等

出　　处：Proceedings of the National Academy of Sciences. 1977 ;74(8):3560-3563.doi:10.1073/pnas.74.8.3560

出版社：The National Academy of Sciences of the United States of America

文章 ID：200594067

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2.Gaucher disease: isolation and comparison of normal and mutant glucocerebrosidase from human spleen tissue

作　　者：P G Pentchev ;R O Brady ;H E Blair 等

出　　处：Proceedings of the National Academy of Sciences. 1978 ;75(8):3970-3973.doi:10.1073/pnas.75.8.3970

出版社：The National Academy of Sciences of the United States of America

文章 ID：200594909

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3.Modification of the blood-brain barrier: increased concentration and fate of enzymes entering the brain

作　　者：J A Barranger ;S I Rapoport ;W R Fredericks 等

出　　处：Proceedings of the National Academy of Sciences. 1979 ;76(1):481-485.doi:10.1073/pnas.76.1.481

出版社：The National Academy of Sciences of the United States of America

文章 ID：200595138

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4.L-glucosylceramide: synthesis, properties, and resistance to catabolism by glucocerebrosidase in vitro

作　　者：A E Gal ;P G Pentchev ;J M Massey 等

出　　处：Proceedings of the National Academy of Sciences. 1979 ;76(7):3083-3086.doi:10.1073/pnas.76.7.3083

出版社：The National Academy of Sciences of the United States of America

文章 ID：200595629

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5.Intracellular trafficking of the free cholesterol derived from LDL cholesteryl ester is defective in vivo in Niemann-Pick C disease: insights on normal metabolism of HDL and LDL gained from the NP-C mutation.

作　　者：R D Shamburek ;P G Pentchev ;L A Zech 等

出　　处：JLR Papers In Press. 1997 ;38(12):2422-2435.

出版社：American Society for Biochemistry and Molecular Biology

文章 ID：192688047

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6.Sphingolipidoses: molecular manifestations and biochemical strategies.

作　　者：P G Pentchev ;J A Barranger

出　　处：JLR Papers In Press. 1978 ;19(4):401-409.

出版社：American Society for Biochemistry and Molecular Biology

文章 ID：192684219

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7.Differential accumulation of cholesterol in Golgi compartments of normal and Niemann-Pick type C fibroblasts incubated with LDL: a cytochemical freeze-fracture study.

作　　者：R A Coxey ;P G Pentchev ;G Campbell 等

出　　处：JLR Papers In Press. 1993 ;34(7):1165-1176.

出版社：American Society for Biochemistry and Molecular Biology

文章 ID：192687203

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8.Cholesterol deprivation affects the fluorescence properties of a ceramide analog at the Golgi apparatus of living cells

作　　者：O C Martin ;M E Comly ;E J Blanchette-Mackie 等

出　　处：Proceedings of the National Academy of Sciences. 1993 ;90(7):2661-2665.doi:10.1073/pnas.90.7.2661

出版社：The National Academy of Sciences of the United States of America

文章 ID：200602206

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	A E Gal	1篇
	C C Schwartz	1篇
	D E Britton	1篇
	E B Neufeld	1篇
	E D Carstea	1篇
	F S Furbish	1篇
	G Campbell	1篇
	H B Brewer	1篇
	J Blanchette-Mackie	1篇
	J K Steusing	1篇
	J M Massey	1篇
	J M VandenBroek	1篇
	J Shiloach	1篇
	K D MacDermot	1篇
	L A Zech	1篇
	M E Comly	1篇
	O C Martin	1篇
	P S Cooper	1篇
	R A Coxey	1篇
	R D Phair	1篇
	R D Shamburek	1篇
	R E Pagano	1篇
	S H Sorrell	1篇
	S I Rapoport	1篇
	W R Fredericks	1篇

	自然科学总论	5篇
	心理学	3篇

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	P G Pentchev	8篇
	R O Brady	5篇
	E J Blanchette-Mackie	2篇
	H E Blair	2篇
	J A Barranger	2篇

	Proceedings of the National Academy of Sciences	5篇
	JLR Papers In Press	3篇

	1997	1篇
	1993	2篇
	1979	2篇
	1978	2篇
	1977	1篇