1.GPI-anchored carbonic anhydrase IV displays both intra- and extracellular activity in cRNA-injected oocytes and in mouse neurons

作　　者：Hans-Peter Schneider ;Marco D. Alt ;Michael Klier 等

出　　处：Proceedings of the National Academy of Sciences. 2013 ;110(4):1494-1499.doi:10.1073/pnas.1221213110

出版社：The National Academy of Sciences of the United States of America

文章 ID：86904118

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2.Carbonic anhydrase XIV is enriched in specific membrane domains of retinal pigment epithelium, Müller cells, and astrocytes

作　　者：Erlend A. Nagelhus ;Thomas M. Mathiisen ;Allen C. Bateman 等

出　　处：Proceedings of the National Academy of Sciences. 2005 ;102(22):8030-8035.doi:10.1073/pnas.0503021102

出版社：The National Academy of Sciences of the United States of America

文章 ID：75176891

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3.Progressive renal injury from transgenic expression of human carbonic anhydrase IV folding mutants is enhanced by deficiency of p58IPK

作　　者：Rupak Datta ;Gul N. Shah ;Timothy S. Rubbelke 等

出　　处：Proceedings of the National Academy of Sciences. 2010 ;107(14):6448-6452.doi:10.1073/pnas.1001905107

出版社：The National Academy of Sciences of the United States of America

文章 ID：200517132

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4.Missense models [Gustm(E536A)Sly, Gustm(E536Q)Sly, and Gustm(L175F)Sly] of murine mucopolysaccharidosis type VII produced by targeted mutagenesis

作　　者：Shunji Tomatsu ;Koji O. Orii ;Carole Vogler 等

出　　处：Proceedings of the National Academy of Sciences. 2002 ;99(23):14982-14987.doi:10.1073/pnas.232570999

出版社：The National Academy of Sciences of the United States of America

文章 ID：200564852

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5.Iron uptake from plasma transferrin by the duodenum is impaired in the Hfe knockout mouse

作　　者：Debbie Trinder ;John K. Olynyk ;William S. Sly 等

出　　处：Proceedings of the National Academy of Sciences. 2002 ;99(8):5622-5626.doi:10.1073/pnas.082112299

出版社：The National Academy of Sciences of the United States of America

文章 ID：200565516

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6.Chemical chaperones protect from effects of apoptosis-inducing mutation in carbonic anhydrase IV identified in retinitis pigmentosa 17

作　　者：Giuseppe Bonapace ;Abdul Waheed ;Gul N. Shah 等

出　　处：Proceedings of the National Academy of Sciences. 2004 ;101(33):12300-12305.doi:10.1073/pnas.0404764101

出版社：The National Academy of Sciences of the United States of America

文章 ID：200590841

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7.Developmentally regulated mannose 6-phosphate receptor-mediated transport of a lysosomal enzyme across the blood-brain barrier

作　　者：Akihiko Urayama ;Jeffrey H. Grubb ;William S. Sly 等

出　　处：Proceedings of the National Academy of Sciences. 2004 ;101(34):12658-12663.doi:10.1073/pnas.0405042101

出版社：The National Academy of Sciences of the United States of America

文章 ID：200590874

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8.Purification and kinetic analysis of recombinant CA XII, a membrane carbonic anhydrase overexpressed in certain cancers

作　　者：Barbara Ulmasov ;Abdul Waheed ;Gul N. Shah 等

出　　处：Proceedings of the National Academy of Sciences. 2000 ;97(26):14212-14217.doi:10.1073/pnas.97.26.14212

出版社：The National Academy of Sciences of the United States of America

文章 ID：200556494

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9.Active site mutant transgene confers tolerance to human β-glucuronidase without affecting the phenotype of MPS VII mice

作　　者：William S. Sly ;Carole Vogler ;Jeffrey H. Grubb 等

出　　处：Proceedings of the National Academy of Sciences. 2001 ;98(5):2205-2210.doi:10.1073/pnas.051623698

出版社：The National Academy of Sciences of the United States of America

文章 ID：200558950

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10.Mouse strain differences determine severity of iron accumulation in Hfe knockout model of hereditary hemochromatosis

作　　者：Robert E. Fleming ;Christopher C. Holden ;Shunji Tomatsu 等

出　　处：Proceedings of the National Academy of Sciences. 2001 ;98(5):2707-2711.doi:10.1073/pnas.051630898

出版社：The National Academy of Sciences of the United States of America

文章 ID：200559036

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	2001	2篇
	2000	1篇
	1999	2篇
	1998	2篇

	Bruce R. Bacon	4篇
	Robert E. Fleming	4篇
	Robert S. Britton	4篇
	Elizabeth M. Brunt	3篇
	Jinxing Jiang	3篇
	Xiao Yan Zhou	3篇
	Carole Vogler	2篇
	Elizabeth M. Snella	2篇
	Giuseppe Bonapace	2篇
	Seppo Parkkila	2篇
	Akihiko Urayama	1篇
	Alan G. Goodman	1篇
	Alena Spiess	1篇
	Allen C. Bateman	1篇
	Alvera Vorster	1篇
	Anna-Kaisa Parkkila	1篇
	Barbara Ulmasov	1篇
	Chingkuang Tu	1篇
	Christopher C. Holden	1篇
	Cynthia E. Prass	1篇
	David A. Ruddy	1篇
	David N. Silverman	1篇
	Debbie Trinder	1篇
	Derry C. Roopenian	1篇
	Dumisani Gama	1篇
	Ekow Oppon	1篇
	Elisabeth Göttert	1篇
	Erlend A. Nagelhus	1篇
	Evan H. Morgan	1篇
	Evi Vollmar	1篇
	Fabian T. Andes	1篇
	Finn-M. Haug	1篇
	George Rebello	1篇
	Gerhard Seitz	1篇
	Hans-Peter Schneider	1篇

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检索条件:"( ( 高级检索(( ((AU:(("William S. Sly")))) )) ) )"

	William S. Sly	15篇
	Abdul Waheed	10篇
	Jeffrey H. Grubb	6篇
	Shunji Tomatsu	6篇
	Gul N. Shah	5篇